6 Its chordae tendineae are generally short and poorly formed. The anterior leaflet is generally redundant and may contain several fenestrations. 16 Used with permission of the Mayo Foundation for Medical Education and Research. Bottom, Tricuspid valve in left-sided Ebstein’s anomaly the displacement of leaflets is similar to that in the right-sided anomaly. Middle, Tricuspid valve in right-sided Ebstein’s anomaly showing displacement of posterior and septal leaflets maximal displacement is at the crux of the posterior and septal leaflets. Top, Normal tricuspid valve with anterior, posterior, and septal leaflets in 1 plane. 6 The spectrum of the malformation in Ebstein’s anomaly may range from only minimal displacement of the septal and posterior leaflets to an imperforate membrane or muscular shelf between the inlet and trabecular zones of the right ventricle.įigure 2. 16 In normal human hearts, the downward displacement of the septal and posterior leaflets in relation to the anterior mitral valve leaflet is <8 mm/m 2 body surface area. 12,15–17 The point of maximal displacement is at the commissure between the posterior and septal leaflets of the tricuspid valve. The apical displacement of the hinge point of the valve in Ebstein’s anomaly from the atrioventricular ring is shown in Figure 2. 12,13 Ebstein’s anomaly is a malformation of the tricuspid valve and right ventricle characterized by (1) adherence of the septal and posterior leaflets to the underlying myocardium (failure of delamination, namely splitting of the tissue by detachment of the inner layer during embryologic development) (2) downward (apical) displacement of the functional annulus (septal>posterior>anterior) (3) dilation of the “atrialized” portion of the right ventricle, with various degrees of hypertrophy and thinning of the wall (4) redundancy, fenestrations, and tethering of the anterior leaflet and (5) dilation of the right atrioventricular junction (true tricuspid annulus). In the normal heart, the tricuspid valve has 3 leaflets: anterior, posterior, and septal. Customer Service and Ordering Information.Stroke: Vascular and Interventional Neurology.Journal of the American Heart Association (JAHA).

Circ: Cardiovascular Quality & Outcomes.Arteriosclerosis, Thrombosis, and Vascular Biology (ATVB).

Anomaly 2 co op